Entry - *139392 - GUANYLATE CYCLASE ACTIVATOR 2A; GUCA2A - OMIM
 
* 139392

GUANYLATE CYCLASE ACTIVATOR 2A; GUCA2A


Alternative titles; symbols

GUCA2
GUANYLIN
GUANYLIN 2, INTESTINAL


HGNC Approved Gene Symbol: GUCA2A

Cytogenetic location: 1p34.2     Genomic coordinates (GRCh38): 1:42,162,690-42,164,745 (from NCBI)


TEXT

Cloning and Expression

Currie et al. (1992) described guanylin, a 15-amino acid peptide purified from rat small intestine, as a potential ligand for intestinal guanylate cyclase. This peptide shares sequence similarity with E. coli heat-stable enterotoxin (STa); see also uroguanylin (601271). The molecular cloning of the human and mouse cDNAs encoding guanylin was reported by de Sauvage et al. (1992). The sequences demonstrated that guanylin is present at the C-terminal end of a larger precursor protein. Expression in mammalian cells indicated that the 94-amino acid proguanylin is inactive. The biologically active guanylin can be released by either chemical or enzymatic treatment of proguanylin. By Northern blot analysis and in situ hybridization, de Sauvage et al. (1992) showed that expression of guanylin mRNA is restricted to cells of the intestinal epithelium, specifically the Paneth cells at the base of the small intestinal crypts. These results demonstrate that guanylin is an endogenous activator of the E. coli heat-stable enterotoxin receptor (STaR).

Wiegand et al. (1992) isolated a cDNA encoding an apparent precursor of guanylin from a human intestinal cDNA library. The mRNA was expressed at high levels in human ileum and colon.

Guanylin is thought to modulate intestinal water/electrolyte transport in a paracrine mode. Hill et al. (1995) reported the nucleotide sequence of the gene, the characteristics of its circulating molecular form, and its localization in enterochromaffin cells of the gut. The hormonal form of guanylin is a 94-amino acid peptide with a molecular mass of 10.3 kD. Guanylin is synthesized by gut enterochromaffin cells as a prohormone of 115 amino acids and is processed to the molecular form of 94 amino acids circulating in the blood.


Gene Structure

Hill et al. (1995) determined that the GUCA2A gene, approximately 2.6 kb in size, consists of 3 exons interrupted by 2 introns.


Mapping

By fluorescence in situ hybridization, Sciaky et al. (1995) mapped the GUCA2 gene to human 1p35-p34. In the mouse, Sciaky et al. (1995) used interspecific backcross analysis to map the Guca2 gene to the distal half of mouse chromosome 4 in a region of homology with human chromosome 1p.


REFERENCES

  1. Currie, M. G., Fok, K. F., Kato, J., Moore, R. J., Hamra, F. K., Duffin, K. L., Smith, C. E. Guanylin: an endogenous activator of intestinal guanylate cyclase. Proc. Nat. Acad. Sci. 89: 947-951, 1992. [PubMed: 1346555, related citations] [Full Text]

  2. de Sauvage, F. J., Keshav, S., Kuang, W.-J., Gillett, N., Henzel, W., Goeddel, D. V. Precursor structure, expression, and tissue distribution of human guanylin. Proc. Nat. Acad. Sci. 89: 9089-9093, 1992. [PubMed: 1409606, related citations] [Full Text]

  3. Hill, O., Kuhn, M., Zucht, H.-D., Cetin, Y., Kulaksiz, H., Adermann, K., Klock, G., Rechkemmer, G., Forssmann, W.-G., Magert, H.-J. Analysis of the human guanylin gene and the processing and cellular localization of the peptide. Proc. Nat. Acad. Sci. 92: 2046-2050, 1995. [PubMed: 7892222, related citations] [Full Text]

  4. Sciaky, D., Jenkins, N. A., Gilbert, D. J., Copeland, N. G., Sonoda, G., Testa, J. R., Cohen, M. B. Mapping of guanylin to murine chromosome 4 and human chromosome 1p34-p35. Genomics 26: 427-429, 1995. [PubMed: 7601480, related citations] [Full Text]

  5. Wiegand, R. C., Kato, J., Huang, M. D., Fok, K. F., Kachur, J. F., Currie, M. G. Human guanylin: cDNA isolation, structure, and activity. FEBS Lett. 311: 150-154, 1992. [PubMed: 1327879, related citations] [Full Text]


Creation Date:
Victor A. McKusick : 10/16/1992
alopez : 02/19/2014
mark : 12/11/1997
terry : 5/22/1996
mark : 5/21/1996
mark : 5/12/1995
terry : 4/18/1995
carol : 10/26/1993
carol : 6/25/1993
carol : 12/14/1992
carol : 10/16/1992

* 139392

GUANYLATE CYCLASE ACTIVATOR 2A; GUCA2A


Alternative titles; symbols

GUCA2
GUANYLIN
GUANYLIN 2, INTESTINAL


HGNC Approved Gene Symbol: GUCA2A

Cytogenetic location: 1p34.2     Genomic coordinates (GRCh38): 1:42,162,690-42,164,745 (from NCBI)


TEXT

Cloning and Expression

Currie et al. (1992) described guanylin, a 15-amino acid peptide purified from rat small intestine, as a potential ligand for intestinal guanylate cyclase. This peptide shares sequence similarity with E. coli heat-stable enterotoxin (STa); see also uroguanylin (601271). The molecular cloning of the human and mouse cDNAs encoding guanylin was reported by de Sauvage et al. (1992). The sequences demonstrated that guanylin is present at the C-terminal end of a larger precursor protein. Expression in mammalian cells indicated that the 94-amino acid proguanylin is inactive. The biologically active guanylin can be released by either chemical or enzymatic treatment of proguanylin. By Northern blot analysis and in situ hybridization, de Sauvage et al. (1992) showed that expression of guanylin mRNA is restricted to cells of the intestinal epithelium, specifically the Paneth cells at the base of the small intestinal crypts. These results demonstrate that guanylin is an endogenous activator of the E. coli heat-stable enterotoxin receptor (STaR).

Wiegand et al. (1992) isolated a cDNA encoding an apparent precursor of guanylin from a human intestinal cDNA library. The mRNA was expressed at high levels in human ileum and colon.

Guanylin is thought to modulate intestinal water/electrolyte transport in a paracrine mode. Hill et al. (1995) reported the nucleotide sequence of the gene, the characteristics of its circulating molecular form, and its localization in enterochromaffin cells of the gut. The hormonal form of guanylin is a 94-amino acid peptide with a molecular mass of 10.3 kD. Guanylin is synthesized by gut enterochromaffin cells as a prohormone of 115 amino acids and is processed to the molecular form of 94 amino acids circulating in the blood.


Gene Structure

Hill et al. (1995) determined that the GUCA2A gene, approximately 2.6 kb in size, consists of 3 exons interrupted by 2 introns.


Mapping

By fluorescence in situ hybridization, Sciaky et al. (1995) mapped the GUCA2 gene to human 1p35-p34. In the mouse, Sciaky et al. (1995) used interspecific backcross analysis to map the Guca2 gene to the distal half of mouse chromosome 4 in a region of homology with human chromosome 1p.


REFERENCES

  1. Currie, M. G., Fok, K. F., Kato, J., Moore, R. J., Hamra, F. K., Duffin, K. L., Smith, C. E. Guanylin: an endogenous activator of intestinal guanylate cyclase. Proc. Nat. Acad. Sci. 89: 947-951, 1992. [PubMed: 1346555] [Full Text: https://doi.org/10.1073/pnas.89.3.947]

  2. de Sauvage, F. J., Keshav, S., Kuang, W.-J., Gillett, N., Henzel, W., Goeddel, D. V. Precursor structure, expression, and tissue distribution of human guanylin. Proc. Nat. Acad. Sci. 89: 9089-9093, 1992. [PubMed: 1409606] [Full Text: https://doi.org/10.1073/pnas.89.19.9089]

  3. Hill, O., Kuhn, M., Zucht, H.-D., Cetin, Y., Kulaksiz, H., Adermann, K., Klock, G., Rechkemmer, G., Forssmann, W.-G., Magert, H.-J. Analysis of the human guanylin gene and the processing and cellular localization of the peptide. Proc. Nat. Acad. Sci. 92: 2046-2050, 1995. [PubMed: 7892222] [Full Text: https://doi.org/10.1073/pnas.92.6.2046]

  4. Sciaky, D., Jenkins, N. A., Gilbert, D. J., Copeland, N. G., Sonoda, G., Testa, J. R., Cohen, M. B. Mapping of guanylin to murine chromosome 4 and human chromosome 1p34-p35. Genomics 26: 427-429, 1995. [PubMed: 7601480] [Full Text: https://doi.org/10.1016/0888-7543(95)80238-h]

  5. Wiegand, R. C., Kato, J., Huang, M. D., Fok, K. F., Kachur, J. F., Currie, M. G. Human guanylin: cDNA isolation, structure, and activity. FEBS Lett. 311: 150-154, 1992. [PubMed: 1327879] [Full Text: https://doi.org/10.1016/0014-5793(92)81387-2]


Creation Date:
Victor A. McKusick : 10/16/1992

Edit History:
alopez : 02/19/2014
mark : 12/11/1997
terry : 5/22/1996
mark : 5/21/1996
mark : 5/12/1995
terry : 4/18/1995
carol : 10/26/1993
carol : 6/25/1993
carol : 12/14/1992
carol : 10/16/1992