. 31.3()


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I                      Phe-          
    Phe
  
II                          Phe-     
  
                                                     

  
III                    
 ,     
                  
        
IV                                 
, 5-, -
        -   - 
         
V                             
, 5-, -
                    
         
VI                                           
    Phe
         
         
         
VII                                          
 C
                        n--
          
        
VIII                     
    Tyr
                                    1. n--
                                       
                                    2. 
                                       
                                            
    Tyr
                                                                         
   
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Tourian A., Sidbury J..: Phenylketonuria and hyperphenylaninemia (. 273) in: Stanbury J.B. et al. (eds): The Metabolic Basis of Inherited Disease, 5th ed. McGraw-Hill, 1983.

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