Indo Y.,1987


Indo Y., Kitano A., Endo F., Akaboshi I., Matsuda I. Altered kinetic properties of the branched-chain a-keto acid de- hydrogenase complex due to mutation of the B-subunit of the branched-chain a-keto acid decarboxylase (E1) component in lym- phoblastoid cells derived from patients with maple syrup urine disease. - J.Clin.Invest., 1987, v. 80, p. 63-70.

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